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adenoid cystic carcinoma, surgical margins, chemotherapy
Primary cutaneous adenoid cystic carcinoma (PCACC) is a rare glandular neoplasm that mimics benign lesions both clinically and histologically making it a diagnostic challenge. Although indolent, ACC has potential for local regional and distant metastasis and even after surgical excision, there is a high recurrence rate. This report outlines a case of a PPACC and reviews current therapeutic approaches.
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