Cutaneous Type Pemphigus Vulgaris of the Scalp: A Rare Unilesional Presentation

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Stefanie Altmann
Adam Chahine
Jarett Casale
Jessica Forbes
Sarah Ferrer-Bruker


pemphigus, vulgaris, isolated, scalp, mucocutaneous, mucous, membrane, cutaneous, acantholysis, acantholytic, PV, autoimmune, mucus, desmoglein


Pemphigus Vulgaris (PV) is the most common subtype of pemphigus, a rare group of autoimmune bullous diseases affecting the skin and mucous membranes. PV can be further subdivided into mucocutaneous and mucosal dominant types, depending on the extent of cutaneous involvement. Almost all cases of PV have mucosal involvement; however, a rare variant of cutaneous-only PV has been reported in the literature. To our knowledge, only two previous accounts of unilesional scalp PV have been reported. We present an unusual case of cutaneous-only PV involving the scalp.


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