Cutaneous Rosai-Dorfman Disease: A Case Report

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Nahla Shihab
Whitney Talbott
Nathalie O Kahn
Erisa Alia
Jeffrey M Weinberg


Cutaneous Rosai-Dorfman disease, Rosai Dorfman disease, histiocytosis


Cutaneous Rosai-Dorfman Disease (CRDD) is an uncommon benign histiocytosis of unknown etiology. CRDD is oftentimes misdiagnosed because it has variable clinical manifestations, particularly in the absence of lymphadenopathy. We report a case of a 23-year-old African American woman presenting with clustered nodular plaques on her right thigh, buttocks, back, and chest for the past two years. History, clinical, histopathological, and immunochemistry findings corresponded with CRDD, and as such, she was treated with halobetasol propionate 0.05% cream twice daily.


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